Congenital Heart Defects - Truncus Arteriosus
 

What’s wrong?

  • One common vessel or trunk from the heart instead of a separate Pulmonary Artery and Aorta.
  • Only one valve between the heart and this trunk
  • The trunk overrides both ventricles, VSD often present
  • Four types:

    • Type I - Main PA branches off the trunk, and then further divides into the RA and left PA.
    • Type II - No MPA
    • Type III - PA comes out of the side of the trunk remote from each other
    • Type IV - Also known as psendotruncus, considered a form of pulmonary atresia with VSD.


Truncus Arteriosus (Type I) with Ventricular Septal Defect, Atrial Septal Defect, Left Aortic Arch Truncus Arteriosus (Type ll-lll) with Ventricular Septal Defect, Atrial Septal Defect, Left Aortic Arch
   
Truncus Arteriosus (Type IV) with Ventricular Septal Defect, Atrial Septal Defect, Left Aortic Arch, Separate Systemic Collaterals to each Lung  
 

Corrective Procedures?

  • Open heart operation
  • Aim of the surgery is to separate PA from aorta and to establish RV-PA continuity using a conduit (Rastelli repair).

What are the possible complications after the procedures?

  • Pulmonary hypertension - may require prolong ventilation
  • Bleeding
  • Arrhythmias
  • Narrowing of heart valve
  • Leaky heart valves