Congenital Heart Defects - Truncus Arteriosus |
What’s wrong?
- One common vessel or trunk from the heart instead of a separate Pulmonary Artery and Aorta.
- Only one valve between the heart and this trunk
- The trunk overrides both ventricles, VSD often present
- Four types:
- Type I - Main PA branches off the trunk, and then further divides into the RA and left PA.
- Type II - No MPA
- Type III - PA comes out of the side of the trunk remote from each other
- Type IV - Also known as psendotruncus, considered a form of pulmonary atresia with VSD.
Truncus Arteriosus (Type I) with Ventricular Septal Defect, Atrial Septal Defect, Left Aortic Arch |
Truncus Arteriosus (Type ll-lll) with Ventricular Septal Defect, Atrial Septal Defect, Left Aortic Arch |
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Truncus Arteriosus (Type IV) with Ventricular Septal Defect, Atrial Septal Defect, Left Aortic Arch, Separate Systemic Collaterals to each Lung |
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Corrective Procedures?
- Open heart operation
- Aim of the surgery is to separate PA from aorta and to establish RV-PA continuity using a conduit (Rastelli repair).
What are the possible complications after the procedures?
- Pulmonary hypertension - may require prolong ventilation
- Bleeding
- Arrhythmias
- Narrowing of heart valve
- Leaky heart valves
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