Congenital Heart Defects - Tricuspid Atresia
with Ventricular Septal Defect, Atrial Septal Defect, Hypoplastic Right Ventricle
 

What’s wrong?

  • Defect present at birth
  • Absence of tricuspid valve
  • RV usually hypoplastic and biventricular repair is not possible
  • Other defects may also be present (ASD,VSD,PS,TGA)

Corrective Procedures?

  1. 1st stage

    • a few days after birth when PDA closes and if oxygen saturation (ie amount of oxygen in body is inadequate)
    • a BT shunt usually needed to be inserted to increase blood flow to the lungs and improve the cyanosis.

  2. 2nd stage - usually less than 2 years old

    • Bidirectional Cavo Pulmonary Connection (BCPC/Glen Procedure)

  3. 3rd stage - usually performed before 3-4 years old

    • Fontan operation - completion of Total CavoPulmonary connection (TCPC)

What are the possible complications after the procedures?

  1. Refer to univentricular section.